Purely extradural spinal nerve root hemangioblastomas
Purely extradural spinal nerve root hemangioblastomas
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Tarih
2016-01-01
Yazarlar
Aytar, Murat Hamit
Yener, Ulas
Eksi, Murat Sakir
Kaya, Behram
Ozgen, Serdar
Sav, Aydin
Alanay, Ahmet
Süreli Yayın başlığı
Süreli Yayın ISSN
Cilt Başlığı
Yayınevi
MEDKNOW PUBLICATIONS \& MEDIA PVT LTD
Dergi Adı
JOURNAL OF CRANIOVERTEBRAL JUNCTION AND SPINE
Özet
Spinal nerve root hemangioblastomas present mostly as intradural-extradurally. Purely extradural spinal nerve root hemangioblastoma is a very rare entity. In this study, we aimed to analyze epidemiological perspectives of purely extradural spinal nerve root hemangioblastomas presented in English medical literature in addition to our own exemplary case. PubMed/MEDLINE was searched using the terms ``hemangioblastoma,{''} ``extradural,{''} ``spinal,{''} and ``nerve root.{''} Demographical variables of age, gender, concomitant presence of von Hippel-Lindau (VHL) disease
spinal imaging and/or intraoperative findings for tumor location were surveyed from retrieved articles. There are 38 patients with purely extradural spinal nerve root hemangioblastoma. The median age is 45 years (range = 24-72 years). Female: male ratio is 0.6. Spinal levels for purely extradural spinal nerve root hemangioblastomas, in order of decreasing frequency, are thoracic (48.6\%), cervical (13.5\%), lumbar (13.5\%), lumbosacral (10.8\%), sacral (8.1\%), and thoracolumbar (5.4\%). Concomitant presence of VHL disease is 45\%. Purely extradural spinal nerve root hemangioblastomas are very rare and can be confused with other more common extradural spinal cord tumors. Concomitant presence of VHL disease is observed in less than half of the patients with purely extradural spinal nerve root hemangioblastomas. Surgery is the first-line treatment in these tumors.
spinal imaging and/or intraoperative findings for tumor location were surveyed from retrieved articles. There are 38 patients with purely extradural spinal nerve root hemangioblastoma. The median age is 45 years (range = 24-72 years). Female: male ratio is 0.6. Spinal levels for purely extradural spinal nerve root hemangioblastomas, in order of decreasing frequency, are thoracic (48.6\%), cervical (13.5\%), lumbar (13.5\%), lumbosacral (10.8\%), sacral (8.1\%), and thoracolumbar (5.4\%). Concomitant presence of VHL disease is 45\%. Purely extradural spinal nerve root hemangioblastomas are very rare and can be confused with other more common extradural spinal cord tumors. Concomitant presence of VHL disease is observed in less than half of the patients with purely extradural spinal nerve root hemangioblastomas. Surgery is the first-line treatment in these tumors.
Açıklama
Anahtar kelimeler
Extradural, hemangioblastoma, spine, surgery, von Hippel-Lindau